Straatsma Syndrome

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File number: 66353


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    1. Linda A Cernichiaro- Espinosa, MD (November 25 2020)

      From
      Oftalmología Integral & RetinaKids MX

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    Rating
    Appears in
    Miscellaneous
    Condition/keywords
    myelinated nerve fibers, high myopia, pediatric retina, leukocoria
    Photographer
    Guillermo Salcedo-Villanueva, MD
    Imaging device
    Zeiss Clarus
    Description
    5-year-old male with leukocoria, high myopia and myelinated nerve fibers (Straatsma Syndrome). OCT showed a foveal depression and intact photoreceptors. Amblyopia management was started.

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