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Vitelliform Macular Dystrophy or Best Disease
Dec 16 2016 by Young Hee Yoon, MD, PhD
Bilateral fundus photographs and autofluorescence images of 15-year-old girl who was diagnosed as vitelliform macular dystrophy or Best disease. Vitelliform macular lesion showed morphologic change during one year.
Photographer: Hyejin Jo, Sunghyun Kim, Heoni Hong, Minjung Chae, Mihwa Shin, Asan medical center, Seoul
Imaging device: Topcon TRC-500X fundus camera, Heidelberg HRA 2 autofluorescence, Heldelberg Spectralis OCT
Condition/keywords: Best disease, pseudohypopyon, scrambled-egg, vitelliform macular dystrophy